| Yeast Systematic Name | Yeast Symbol | SGDID | Analog Name | Analog Description | EC | Organism | Disease | Structure | Uniprot | Human ID | Human Symbol | HHsearch Probability | HHsearch E_value | HHsearch P_value | HHsearch Score | Flag Disease related | Flag Homo sapiens | Flag Mus musculus | Flag Danio rerio | Flag Drosophila melanogaster | Flag Caenorhabditis elegans | Flag Arabidopsis thaliana | Flag Escherichia coli |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| YER178W | PDA1 | SGDID:S000000980 | pdhA |
Pyruvate dehydrogenase E1 component subunit alpha (EC 1.2.4.1) |
1.2.4.1 | Geobacillus stearothermophilus | 1w85_a | P21873 | 100.00 | 8.10E-63 | 6.00E-67 | 484.40 | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 0 | |||
| YER178W | PDA1 | SGDID:S000000980 | PDHA1 PHE1A |
Pyruvate dehydrogenase E1 component subunit alpha, somatic form, mitochondrial (EC 1.2.4.1) (PDHE1-A type I) |
1.2.4.1 | Homo sapiens | Episodic Ataxia,Leigh Syndrome With Leukodystrophy,Periventricular Leukomalacia,Dystonia,Marshall-Smith Syndrome,Lactic Acidosis,Pyruvate Dehydrogenase E3-Binding Protein Deficiency,Coffin-Lowry Syndrome,Mitochondrial Complex I Deficiency, Nuclear Type 1,Alpha-Ketoglutarate Dehydrogenase Deficiency,Pyruvate Dehydrogenase E1-Alpha Deficiency,Leigh Syndrome |
2ozl_a | P08559 | ENSG00000131828 | PDHA1 | 100.00 | 1.70E-51 | 1.30E-55 | 407.10 | 1 | 1 | 0 | 0 | 0 | 0 | 0 | 0 |
| YER178W | PDA1 | SGDID:S000000980 | BCKDHA |
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial (EC 1.2.4.4) (Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain) (BCKDE1A) (BCKDH E1-alpha) |
1.2.4.4 | Homo sapiens | Amino Acid Metabolic Disorder,Branched-Chain Keto Acid Dehydrogenase Kinase Deficiency,Intermediate Maple Syrup Urine Disease,Methylmalonic Acidemia,Propionic Acidemia,Maple Syrup Urine Disease,Organic Acidemia |
2bfd_a | P12694 | ENSG00000248098 | BCKDHA | 100.00 | 2.70E-54 | 2.00E-58 | 431.40 | 1 | 1 | 0 | 0 | 0 | 0 | 0 | 0 |
| YER178W | PDA1 | SGDID:S000000980 | pdhA |
Pyruvate dehydrogenase E1 component subunit alpha (EC 1.2.4.1) |
1.2.4.1 | Geobacillus stearothermophilus | 1w85_g | P21873 | 100.00 | 3.80E-49 | 2.90E-53 | 390.40 | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |